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ABCB11

receptor: FXRTier 1

Drug substrates

drugs causing cholestasis (bosentan, cyclosporine, estrogens)

refs: 25198545

CAMIP causal chains

FXR

Disrupted receptor-mediated transactivation via the FXR/RXRα heterodimer, abolishing the critical canalicular expression of the Bile Salt Export Pump. This directly cripples the ATP-dependent rate-limiting step of hepatic bile acid elimination, precipitating toxic intracellular bile salt accumulation and rendering hepatocytes profoundly vulnerable to severe drug-induced cholestatic liver injury under medications such as bosentan and cyclosporine.

Affected substrate drugs (PharmGKB): bosentan; cyclosporine; estrogens

Scored variants near ABCB11

chr2:168,820,780..169,131,324, gene body plus 100 kb. Showing the strongest 200 by effect size.

Variant Position PXR FXR AhR AF
chr2_169031334_A_Gchr2:1690313341.0001.0000.916—   
chr2_169031340_A_Gchr2:1690313401.0001.0000.910—   
chr2_169031312_T_Achr2:1690313120.5721.0001.000—   
chr2_169031342_T_Cchr2:1690313420.8080.9770.713—   
chr2_169031312_T_Gchr2:1690313120.5020.9081.000—   
chr2_169031317_A_Gchr2:1690313170.5410.7180.461—   
chr2_169031343_C_Gchr2:1690313430.4840.5390.531—   
chr2_169031315_T_Gchr2:1690313150.4610.7460.663—   
chr2_169031224_C_Gchr2:169031224-0.403-0.597-0.590—   
chr2_169031254_G_Tchr2:1690312540.4020.4810.275—   
chr2_169031341_T_Gchr2:1690313410.4020.6050.303—   
chr2_169031224_C_Achr2:169031224-0.398-0.576-0.632—   
chr2_169031223_A_Cchr2:169031223-0.357-0.504-0.640—   
chr2_169031326_A_Tchr2:169031326-0.369-0.542-0.506—   
chr2_169031282_A_Cchr2:1690312820.3610.5570.287—   
chr2_169031338_G_Tchr2:169031338-0.353-0.544-0.393—   
chr2_169031225_C_Achr2:169031225-0.348-0.499-0.435—   
chr2_169031223_A_Tchr2:169031223-0.346-0.469-0.573—   
chr2_169031288_T_Cchr2:169031288-0.275-0.487-0.584—   
chr2_169031308_T_Cchr2:1690313080.3390.4890.303—   
chr2_169031288_T_Achr2:169031288-0.282-0.471-0.570—   
chr2_169031290_T_Cchr2:169031290-0.328-0.640-0.483—   
chr2_169031315_T_Cchr2:169031315-0.325-0.499-0.514—   
chr2_169031314_T_Cchr2:169031314-0.312-0.514-0.433—   
chr2_169031312_T_Cchr2:1690313120.3020.4140.483—   
chr2_169031295_A_Tchr2:169031295-0.193-0.320-0.486—   
chr2_169031313_T_Cchr2:169031313-0.267-0.423-0.483—   
chr2_169031224_C_Tchr2:169031224-0.280-0.471-0.461—   
chr2_169031292_A_Gchr2:1690312920.2740.5470.410—   
chr2_169031294_A_Tchr2:169031294-0.207-0.484-0.466—   
chr2_169031336_C_Gchr2:169031336-0.267-0.344-0.452—   
chr2_169031338_G_Achr2:169031338-0.265-0.355-0.253—   
chr2_169031291_C_Tchr2:169031291-0.222-0.426-0.449—   
chr2_169031289_T_Achr2:169031289-0.215-0.458-0.441—   
chr2_169031302_C_Gchr2:1690313020.2570.5090.399—   
chr2_169031336_C_Achr2:169031336-0.220-0.225-0.427—   
chr2_169031262_G_Cchr2:1690312620.2430.2700.225—   
chr2_169031223_A_Gchr2:169031223-0.241-0.348-0.379—   
chr2_169031194_G_Cchr2:1690311940.2390.2540.149—   
chr2_169031308_T_Gchr2:1690313080.2390.4430.388—   
chr2_169031340_A_Tchr2:1690313400.2390.2800.275—   
chr2_169031296_C_Achr2:169031296-0.148-0.306-0.407—   
chr2_169031254_G_Cchr2:1690312540.2360.2750.169—   
chr2_169031334_A_Tchr2:169031334-0.231-0.320-0.275—   
chr2_169031293_C_Gchr2:169031293-0.164-0.428-0.393—   
chr2_169031294_A_Gchr2:169031294-0.135-0.358-0.393—   
chr2_169031333_G_Tchr2:169031333-0.227-0.325-0.281—   
chr2_169031291_C_Gchr2:169031291-0.175-0.378-0.388—   
chr2_169031325_A_Tchr2:169031325-0.225-0.297-0.309—   
chr2_169031317_A_Tchr2:169031317-0.225-0.312-0.315—   
chr2_169031288_T_Gchr2:169031288-0.137-0.271-0.379—   
chr2_169031306_C_Tchr2:169031306-0.216-0.353-0.301—   
chr2_169031331_C_Achr2:169031331-0.196-0.262-0.365—   
chr2_169031309_C_Tchr2:169031309-0.211-0.319-0.264—   
chr2_169031226_T_Cchr2:169031226-0.210-0.270-0.202—   
chr2_169031226_T_Achr2:169031226-0.208-0.295-0.174—   
chr2_169031329_C_Achr2:169031329-0.208-0.262-0.216—   
chr2_169031225_C_Tchr2:169031225-0.207-0.302-0.174—   
chr2_169031341_T_Achr2:1690313410.2070.1440.225—   
chr2_169031324_T_Cchr2:1690313240.1990.2950.129—   
chr2_169031198_T_Gchr2:169031198-0.192-0.217-0.146—   
chr2_169031290_T_Gchr2:1690312900.1900.2440.191—   
chr2_169031291_C_Achr2:169031291-0.151-0.348-0.326—   
chr2_169031336_C_Tchr2:169031336-0.189-0.236-0.289—   
chr2_169031343_C_Achr2:169031343-0.184-0.190-0.239—   
chr2_169031322_T_Achr2:1690313220.1810.2220.180—   
chr2_169031184_A_Cchr2:1690311840.1800.1740.253—   
chr2_169031270_C_Tchr2:169031270-0.180-0.237-0.124—   
chr2_169031292_A_Tchr2:169031292-0.175-0.330-0.309—   
chr2_169031289_T_Cchr2:169031289-0.106-0.282-0.306—   
chr2_169031342_T_Achr2:1690313420.1790.2090.197—   
chr2_169031304_A_Cchr2:169031304-0.177-0.248-0.242—   
chr2_169031320_A_Cchr2:169031320-0.167-0.297-0.301—   
chr2_169031294_A_Cchr2:169031294-0.123-0.345-0.298—   
chr2_169031321_T_Achr2:169031321-0.166-0.327-0.289—   
chr2_169031260_A_Tchr2:1690312600.1660.1360.135—   
chr2_169031296_C_Gchr2:169031296-0.108-0.191-0.281—   
chr2_169031313_T_Achr2:169031313-0.144-0.227-0.278—   
chr2_169031314_T_Achr2:169031314-0.055-0.277-0.278—   
chr2_169031309_C_Achr2:169031309-0.160-0.297-0.185—   
chr2_169031289_T_Gchr2:169031289-0.131-0.315-0.272—   
chr2_169031225_C_Gchr2:169031225-0.156-0.222-0.037—   
chr2_169031323_C_Achr2:169031323-0.143-0.247-0.267—   
chr2_169031339_A_Gchr2:1690313390.1550.1890.185—   
chr2_169031290_T_Achr2:1690312900.1510.1660.174—   
chr2_169031293_C_Achr2:169031293-0.134-0.290-0.258—   
chr2_169031327_A_Tchr2:169031327-0.135-0.149-0.258—   
chr2_169031176_T_Achr2:1690311760.1490.1310.098—   
chr2_169031267_C_Gchr2:1690312670.1490.2170.247—   
chr2_169031178_A_Cchr2:1690311780.1480.1660.115—   
chr2_169031226_T_Gchr2:169031226-0.148-0.166-0.135—   
chr2_169031295_A_Cchr2:169031295-0.121-0.252-0.253—   
chr2_169031327_A_Gchr2:169031327-0.148-0.150-0.211—   
chr2_169031329_C_Gchr2:169031329-0.148-0.184-0.171—   
chr2_169031332_T_Achr2:169031332-0.123-0.270-0.253—   
chr2_169031310_G_Achr2:169031310-0.147-0.229-0.169—   
chr2_169031278_A_Gchr2:1690312780.1430.1740.202—   
chr2_169031324_T_Gchr2:1690313240.1390.2490.219—   
chr2_169031279_G_Cchr2:169031279-0.138-0.154-0.177—   
chr2_169031292_A_Cchr2:169031292-0.138-0.307-0.230—   
chr2_169031197_T_Cchr2:169031197-0.134-0.0600.087—   
chr2_169031305_A_Tchr2:169031305-0.134-0.204-0.219—   
chr2_169031308_T_Achr2:1690313080.1210.1590.230—   
chr2_169031264_A_Cchr2:169031264-0.134-0.151-0.022—   
chr2_169031316_C_Achr2:1690313160.1310.0280.073—   
chr2_169031332_T_Gchr2:169031332-0.125-0.234-0.225—   
chr2_169031311_G_Achr2:169031311-0.130-0.139-0.157—   
chr2_169031306_C_Achr2:169031306-0.129-0.234-0.157—   
chr2_169031222_T_Gchr2:169031222-0.116-0.257-0.219—   
chr2_169031316_C_Tchr2:169031316-0.075-0.254-0.219—   
chr2_169031335_A_Cchr2:1690313350.1250.2070.185—   
chr2_169031171_A_Cchr2:1690311710.1250.1010.110—   
chr2_169031315_T_Achr2:1690313150.1250.1690.112—   
chr2_169031337_A_Cchr2:1690313370.1250.1640.062—   
chr2_169031179_A_Cchr2:1690311790.1230.0630.076—   
chr2_169031335_A_Tchr2:169031335-0.123-0.189-0.191—   
chr2_169031188_G_Tchr2:169031188-0.110-0.123-0.208—   
chr2_169031313_T_Gchr2:169031313-0.085-0.176-0.208—   
chr2_169031318_T_Cchr2:169031318-0.121-0.217-0.118—   
chr2_169031311_G_Cchr2:169031311-0.120-0.173-0.169—   
chr2_169031307_C_Tchr2:169031307-0.099-0.174-0.205—   
chr2_169031295_A_Gchr2:169031295-0.034-0.161-0.202—   
chr2_169031339_A_Cchr2:1690313390.1180.1790.051—   
chr2_169031326_A_Gchr2:1690313260.1170.1540.101—   
chr2_169031326_A_Cchr2:1690313260.1160.1560.146—   
chr2_169031260_A_Cchr2:1690312600.1150.0930.118—   
chr2_169031227_G_Cchr2:169031227-0.113-0.128-0.112—   
chr2_169031266_T_Cchr2:169031266-0.113-0.176-0.096—   
chr2_169008089_G_Tchr2:169008089-0.1120.0400.110—   
chr2_169031287_G_Tchr2:169031287-0.034-0.108-0.191—   
chr2_169031317_A_Cchr2:169031317-0.111-0.222-0.152—   
chr2_169031172_A_Cchr2:1690311720.1100.0930.107—   
chr2_169031241_G_Tchr2:1690312410.1100.1110.143—   
chr2_169031276_A_Tchr2:169031276-0.110-0.1840.039—   
chr2_169008129_G_Cchr2:1690081290.057-0.045-0.187—   
chr2_169031258_T_Cchr2:169031258-0.108-0.0910.006—   
chr2_169031263_G_Cchr2:1690312630.0900.1410.185—   
chr2_169031302_C_Tchr2:169031302-0.107-0.121-0.135—   
chr2_169031304_A_Tchr2:169031304-0.106-0.168-0.135—   
chr2_169031323_C_Tchr2:169031323-0.106-0.146-0.132—   
chr2_169031194_G_Tchr2:1690311940.1050.1080.039—   
chr2_169031307_C_Gchr2:169031307-0.068-0.083-0.180—   
chr2_169031232_T_Gchr2:169031232-0.084-0.106-0.177—   
chr2_169031337_A_Tchr2:1690313370.1020.1260.079—   
chr2_169031299_T_Cchr2:169031299-0.100-0.161-0.174—   
chr2_169031330_A_Gchr2:1690313300.1020.1410.073—   
chr2_169031247_G_Tchr2:1690312470.1000.1180.048—   
chr2_169031301_T_Cchr2:1690313010.1000.1740.140—   
chr2_169031307_C_Achr2:169031307-0.095-0.154-0.171—   
chr2_169031245_A_Cchr2:1690312450.0980.1180.087—   
chr2_169031267_C_Achr2:1690312670.0980.0830.118—   
chr2_169031333_G_Cchr2:169031333-0.076-0.123-0.169—   
chr2_169008119_T_Achr2:1690081190.0980.063-0.006—   
chr2_169031311_G_Tchr2:169031311-0.098-0.110-0.138—   
chr2_169031216_G_Tchr2:1690312160.0970.1130.104—   
chr2_169031298_T_Cchr2:169031298-0.096-0.139-0.056—   
chr2_169031194_G_Achr2:1690311940.0950.101-0.003—   
chr2_169031231_A_Cchr2:169031231-0.095-0.086-0.039—   
chr2_169031259_A_Gchr2:169031259-0.095-0.141-0.076—   
chr2_169031280_T_Achr2:169031280-0.033-0.118-0.163—   
chr2_169031284_A_Gchr2:169031284-0.084-0.101-0.163—   
chr2_169031330_A_Cchr2:1690313300.0940.2090.163—   
chr2_169031186_G_Cchr2:1690311860.0930.0710.062—   
chr2_169031298_T_Achr2:169031298-0.093-0.161-0.107—   
chr2_169031325_A_Gchr2:1690313250.0930.1460.107—   
chr2_169031227_G_Tchr2:169031227-0.092-0.071-0.096—   
chr2_169031235_G_Tchr2:1690312350.0920.1030.090—   
chr2_169031241_G_Cchr2:1690312410.0920.1510.132—   
chr2_169031252_A_Cchr2:169031252-0.092-0.144-0.079—   
chr2_169031263_G_Tchr2:1690312630.0850.1560.157—   
chr2_169031278_A_Cchr2:169031278-0.092-0.118-0.017—   
chr2_169031173_G_Achr2:1690311730.0900.1280.006—   
chr2_169031227_G_Achr2:169031227-0.090-0.093-0.076—   
chr2_169031244_G_Achr2:1690312440.0900.0880.079—   
chr2_169031244_G_Cchr2:1690312440.0900.1060.112—   
chr2_169031176_T_Gchr2:1690311760.0890.0830.090—   
chr2_169031180_A_Tchr2:169031180-0.089-0.113-0.079—   
chr2_169031287_G_Achr2:1690312870.0890.1940.152—   
chr2_169031293_C_Tchr2:169031293-0.043-0.108-0.152—   
chr2_169008140_T_Gchr2:169008140-0.0870.005-0.004—   
chr2_169031239_T_Cchr2:1690312390.0870.1230.059—   
chr2_169031299_T_Gchr2:1690312990.0870.0230.067—   
chr2_169008089_G_Achr2:169008089-0.0850.0180.045—   
chr2_169031318_T_Gchr2:169031318-0.084-0.136-0.118—   
chr2_169031174_A_Cchr2:1690311740.0840.0530.090—   
chr2_169031251_G_Tchr2:169031251-0.070-0.113-0.143—   
chr2_169031283_A_Tchr2:169031283-0.084-0.121-0.129—   
chr2_169008120_C_Tchr2:1690081200.0830.015-0.074—   
chr2_169008090_A_Tchr2:169008090-0.0820.0100.079—   
chr2_169031177_T_Gchr2:1690311770.0820.0680.093—   
chr2_169031200_G_Tchr2:1690312000.0820.065-0.031—   
chr2_169031220_C_Achr2:169031220-0.082-0.164-0.017—   
chr2_169031220_C_Tchr2:1690312200.0380.0100.140—   
chr2_169031236_A_Cchr2:1690312360.0110.0450.140—   
chr2_169031304_A_Gchr2:1690313040.0820.1910.104—   
chr2_169031167_A_Cchr2:1690311670.0800.0430.096—   
chr2_169031173_G_Cchr2:1690311730.0800.0600.039—   
chr2_169031278_A_Tchr2:169031278-0.080-0.081-0.051—   
chr2_169031320_A_Gchr2:169031320-0.047-0.121-0.138—   
chr2_169031303_C_Tchr2:1690313030.0800.1210.084—   

Showing 200 of 200 in this window. Scores are the p99-scaled [−1, 1] value; click a column to sort.