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ABCB4

receptor: FXRTier 1

Drug substrates

cholestasis/gallstone risk (intrahepatic cholestasis of pregnancy)

refs: 25198545

CAMIP causal chains

FXR

Disrupted receptor-mediated transactivation via the FXR/RXRα heterodimer, impairing the coordinated up-regulation of ABCB4. This leads to a deficiency in ATP-dependent phospholipid translocation across the canalicular membrane of hepatocytes, decreasing biliary phospholipid secretion and increasing the physiological susceptibility to intrahepatic cholestasis and gallstone formation.

Affected substrate drugs (PharmGKB): imatinib; anthracyclines and related substances

Scored variants near ABCB4

chr7:87,301,695..87,575,703, gene body plus 100 kb. Showing the strongest 200 by effect size.

Variant Position PXR FXR AhR AF
chr7_87463645_A_Cchr7:874636450.4460.6080.507—   
chr7_87463682_A_Cchr7:874636820.2210.2830.250—   
chr7_87464039_A_Gchr7:87464039-0.219-0.327-0.183—   
chr7_87463678_C_Achr7:874636780.1810.3060.195—   
chr7_87463645_A_Tchr7:874636450.1680.2440.208—   
chr7_87463649_A_Cchr7:87463649-0.123-0.153-0.144—   
chr7_87463649_A_Gchr7:87463649-0.115-0.140-0.107—   
chr7_87463689_G_Cchr7:874636890.1150.1510.195—   
chr7_87463681_T_Achr7:87463681-0.109-0.151-0.134—   
chr7_87464029_T_Cchr7:87464029-0.101-0.096-0.110—   
chr7_87463690_T_Cchr7:874636900.0890.1350.177—   
chr7_87463706_A_Cchr7:874637060.0700.0780.171—   
chr7_87464007_T_Achr7:87464007-0.094-0.109-0.085—   
chr7_87463680_G_Cchr7:87463680-0.091-0.114-0.092—   
chr7_87463680_G_Achr7:87463680-0.089-0.101-0.113—   
chr7_87463678_C_Gchr7:874636780.0870.1560.070—   
chr7_87463638_A_Tchr7:874636380.0840.1320.092—   
chr7_87463649_A_Tchr7:87463649-0.084-0.109-0.092—   
chr7_87463713_T_Achr7:87463713-0.084-0.0830.015—   
chr7_87463681_T_Cchr7:87463681-0.080-0.135-0.031—   
chr7_87463681_T_Gchr7:87463681-0.080-0.117-0.064—   
chr7_87463991_T_Achr7:874639910.0800.0650.018—   
chr7_87464044_T_Achr7:87464044-0.080-0.101-0.012—   
chr7_87463618_G_Achr7:87463618-0.026-0.031-0.140—   
chr7_87463650_C_Achr7:874636500.0790.0520.012—   
chr7_87463683_C_Achr7:87463683-0.079-0.109-0.076—   
chr7_87463696_A_Cchr7:874636960.0360.0310.140—   
chr7_87464036_T_Cchr7:874640360.0790.0780.037—   
chr7_87463680_G_Tchr7:87463680-0.077-0.078-0.110—   
chr7_87464012_A_Gchr7:87464012-0.077-0.0470.049—   
chr7_87463641_C_Achr7:874636410.0750.1430.107—   
chr7_87463665_T_Gchr7:874636650.0410.0750.134—   
chr7_87463668_C_Tchr7:87463668-0.075-0.070-0.085—   
chr7_87463707_G_Cchr7:874637070.0750.0440.052—   
chr7_87464001_T_Gchr7:874640010.0070.0680.134—   
chr7_87463644_A_Gchr7:874636440.0620.0860.131—   
chr7_87463683_C_Gchr7:87463683-0.074-0.106-0.061—   
chr7_87463712_A_Cchr7:874637120.021-0.0050.128—   
chr7_87463995_C_Tchr7:874639950.0720.106-0.012—   
chr7_87463648_A_Tchr7:87463648-0.070-0.078-0.049—   
chr7_87463677_A_Cchr7:87463677-0.070-0.094-0.061—   
chr7_87463666_T_Gchr7:874636660.0240.0440.122—   
chr7_87463697_G_Cchr7:874636970.0650.0650.122—   
chr7_87463712_A_Gchr7:87463712-0.009-0.0050.122—   
chr7_87463995_C_Gchr7:874639950.0500.1350.122—   
chr7_87464004_A_Cchr7:874640040.0530.0910.122—   
chr7_87464042_G_Tchr7:87464042-0.068-0.075-0.110—   
chr7_87463664_A_Cchr7:874636640.0020.0340.119—   
chr7_87463694_A_Cchr7:874636940.0360.0360.119—   
chr7_87463624_A_Tchr7:87463624-0.065-0.057-0.064—   
chr7_87463647_T_Achr7:87463647-0.065-0.094-0.095—   
chr7_87463665_T_Cchr7:874636650.0290.0620.113—   
chr7_87463679_A_Cchr7:87463679-0.063-0.094-0.043—   
chr7_87463698_G_Cchr7:874636980.0630.0440.092—   
chr7_87463710_A_Cchr7:874637100.027-0.0080.113—   
chr7_87464003_T_Achr7:874640030.0630.0910.037—   
chr7_87463617_G_Achr7:874636170.0620.0700.052—   
chr7_87463679_A_Tchr7:87463679-0.062-0.086-0.101—   
chr7_87463692_G_Cchr7:874636920.0560.0440.110—   
chr7_87464003_T_Cchr7:874640030.0620.0880.055—   
chr7_87464023_C_Gchr7:87464023-0.062-0.083-0.024—   
chr7_87464026_T_Cchr7:87464026-0.062-0.062-0.067—   
chr7_87464031_T_Cchr7:87464031-0.062-0.044-0.049—   
chr7_87464038_A_Tchr7:87464038-0.062-0.099-0.067—   
chr7_87464043_C_Achr7:874640430.0620.1040.012—   
chr7_87463676_C_Tchr7:87463676-0.060-0.073-0.070—   
chr7_87463677_A_Gchr7:87463677-0.060-0.083-0.027—   
chr7_87463683_C_Tchr7:87463683-0.060-0.106-0.089—   
chr7_87463699_A_Gchr7:87463699-0.060-0.010-0.018—   
chr7_87464000_C_Achr7:874640000.0600.052-0.018—   
chr7_87464012_A_Tchr7:87464012-0.060-0.0210.024—   
chr7_87464033_T_Cchr7:87464033-0.060-0.060-0.024—   
chr7_87463618_G_Tchr7:874636180.0580.0750.064—   
chr7_87463622_C_Achr7:874636220.0580.0550.009—   
chr7_87463641_C_Tchr7:87463641-0.029-0.039-0.104—   
chr7_87463714_A_Gchr7:87463714-0.058-0.0650.018—   
chr7_87463719_G_Achr7:87463719-0.002-0.013-0.104—   
chr7_87464011_T_Cchr7:87464011-0.058-0.099-0.031—   
chr7_87464020_T_Cchr7:87464020-0.058-0.0520.024—   
chr7_87464024_T_Cchr7:87464024-0.058-0.023-0.006—   
chr7_87463637_A_Cchr7:874636370.0220.0570.101—   
chr7_87463647_T_Gchr7:87463647-0.056-0.104-0.043—   
chr7_87463713_T_Cchr7:87463713-0.022-0.0360.101—   
chr7_87463991_T_Cchr7:874639910.0560.0520.055—   
chr7_87463999_T_Gchr7:874639990.0560.0440.061—   
chr7_87464001_T_Achr7:874640010.0560.0420.067—   
chr7_87464017_T_Cchr7:87464017-0.056-0.0620.018—   
chr7_87463664_A_Gchr7:87463664-0.0050.0230.098—   
chr7_87463669_T_Gchr7:874636690.0550.0750.082—   
chr7_87463676_C_Gchr7:87463676-0.055-0.078-0.082—   
chr7_87463700_T_Cchr7:874637000.0210.0780.098—   
chr7_87463714_A_Cchr7:874637140.0050.0050.098—   
chr7_87463990_A_Gchr7:874639900.0220.0440.098—   
chr7_87463991_T_Gchr7:874639910.0550.0570.061—   
chr7_87463996_A_Gchr7:874639960.0090.0730.098—   
chr7_87464012_A_Cchr7:87464012-0.055-0.0310.012—   
chr7_87464015_T_Gchr7:874640150.0140.0260.098—   
chr7_87464032_C_Tchr7:87464032-0.055-0.049-0.073—   
chr7_87464033_T_Gchr7:874640330.0530.0620.098—   
chr7_87463641_C_Gchr7:874636410.0410.0940.095—   
chr7_87463660_T_Gchr7:874636600.0530.0940.046—   
chr7_87463676_C_Achr7:87463676-0.053-0.057-0.082—   
chr7_87463693_G_Cchr7:874636930.0460.0310.095—   
chr7_87463716_A_Cchr7:874637160.0530.0600.092—   
chr7_87463607_A_Cchr7:87463607-0.010-0.0310.092—   
chr7_87463617_G_Tchr7:874636170.010-0.031-0.092—   
chr7_87463647_T_Cchr7:874636470.0510.0550.064—   
chr7_87463660_T_Cchr7:874636600.0260.0160.092—   
chr7_87463708_A_Cchr7:874637080.0100.0000.092—   
chr7_87464006_C_Gchr7:87464006-0.051-0.073-0.067—   
chr7_87464042_G_Achr7:87464042-0.051-0.075-0.079—   
chr7_87463684_A_Tchr7:87463684-0.043-0.086-0.089—   
chr7_87463688_T_Gchr7:87463688-0.050-0.042-0.021—   
chr7_87463703_T_Cchr7:87463703-0.050-0.0440.040—   
chr7_87463987_T_Achr7:874639870.0500.0680.018—   
chr7_87464034_T_Gchr7:874640340.0500.0210.049—   
chr7_87463584_A_Cchr7:874635840.0340.0160.085—   
chr7_87463654_T_Cchr7:87463654-0.010-0.031-0.085—   
chr7_87463657_C_Achr7:87463657-0.046-0.039-0.085—   
chr7_87463677_A_Tchr7:87463677-0.048-0.081-0.085—   
chr7_87463682_A_Tchr7:874636820.0480.1060.058—   
chr7_87463688_T_Achr7:87463688-0.048-0.057-0.058—   
chr7_87463695_G_Cchr7:874636950.0480.0600.082—   
chr7_87463996_A_Cchr7:874639960.0480.0620.043—   
chr7_87464024_T_Gchr7:87464024-0.0220.0030.085—   
chr7_87464040_A_Cchr7:874640400.048-0.0030.031—   
chr7_87464041_T_Cchr7:874640410.0480.0490.061—   
chr7_87463613_A_Cchr7:874636130.0260.0310.082—   
chr7_87463657_C_Gchr7:87463657-0.043-0.044-0.082—   
chr7_87463659_G_Cchr7:874636590.0460.0490.067—   
chr7_87463667_C_Gchr7:874636670.0100.0620.082—   
chr7_87463690_T_Achr7:87463690-0.046-0.060-0.003—   
chr7_87463696_A_Tchr7:874636960.0460.0780.040—   
chr7_87463713_T_Gchr7:87463713-0.046-0.0420.082—   
chr7_87463718_G_Cchr7:874637180.0460.0600.018—   
chr7_87464002_A_Cchr7:874640020.0460.0700.067—   
chr7_87464026_T_Achr7:87464026-0.046-0.016-0.067—   
chr7_87463642_T_Gchr7:87463642-0.044-0.0620.018—   
chr7_87463717_A_Cchr7:874637170.0380.0440.079—   
chr7_87464003_T_Gchr7:874640030.0440.0600.024—   
chr7_87464013_T_Achr7:874640130.0440.0180.006—   
chr7_87399457_A_Cchr7:873994570.008-0.0030.076—   
chr7_87399461_T_Cchr7:87399461-0.008-0.0050.076—   
chr7_87463605_T_Cchr7:87463605-0.021-0.0180.076—   
chr7_87463619_T_Cchr7:874636190.0430.0000.021—   
chr7_87463645_A_Gchr7:874636450.0120.0420.076—   
chr7_87463646_G_Achr7:87463646-0.022-0.010-0.076—   
chr7_87463655_G_Tchr7:87463655-0.041-0.055-0.076—   
chr7_87463656_G_Tchr7:87463656-0.022-0.023-0.076—   
chr7_87463663_A_Cchr7:874636630.0120.0100.076—   
chr7_87463679_A_Gchr7:87463679-0.043-0.052-0.015—   
chr7_87463684_A_Gchr7:87463684-0.043-0.078-0.006—   
chr7_87463711_G_Achr7:87463711-0.043-0.034-0.009—   
chr7_87463712_A_Tchr7:87463712-0.015-0.0080.076—   
chr7_87464009_C_Achr7:874640090.0430.0290.012—   
chr7_87464018_T_Cchr7:87464018-0.043-0.0420.031—   
chr7_87464031_T_Achr7:87464031-0.043-0.044-0.024—   
chr7_87464037_A_Gchr7:874640370.0430.0940.012—   
chr7_87463612_A_Cchr7:874636120.0410.0550.061—   
chr7_87463666_T_Cchr7:874636660.0150.0600.073—   
chr7_87463690_T_Gchr7:87463690-0.039-0.047-0.073—   
chr7_87463710_A_Gchr7:87463710-0.041-0.0490.040—   
chr7_87463989_C_Tchr7:87463989-0.014-0.003-0.073—   
chr7_87464002_A_Gchr7:874640020.0340.0570.073—   
chr7_87464013_T_Gchr7:874640130.0260.0290.073—   
chr7_87464032_C_Achr7:87464032-0.041-0.026-0.055—   
chr7_87399442_T_Achr7:873994420.0200.0520.070—   
chr7_87463636_G_Tchr7:874636360.0270.0650.070—   
chr7_87463662_G_Cchr7:874636620.0000.0360.070—   
chr7_87463678_C_Tchr7:874636780.0390.0700.024—   
chr7_87463700_T_Gchr7:87463700-0.039-0.0050.049—   
chr7_87463706_A_Gchr7:87463706-0.039-0.0340.000—   
chr7_87463992_T_Gchr7:874639920.0390.0080.049—   
chr7_87464014_C_Tchr7:874640140.0390.013-0.018—   
chr7_87463593_A_Cchr7:874635930.0380.0550.064—   
chr7_87463617_G_Cchr7:874636170.0380.018-0.009—   
chr7_87463626_A_Tchr7:874636260.0360.0390.067—   
chr7_87463637_A_Gchr7:87463637-0.038-0.005-0.021—   
chr7_87463658_A_Gchr7:87463658-0.034-0.0310.067—   
chr7_87463666_T_Achr7:87463666-0.0090.0600.067—   
chr7_87463675_G_Achr7:87463675-0.031-0.052-0.067—   
chr7_87463692_G_Tchr7:874636920.0380.0310.040—   
chr7_87463718_G_Tchr7:874637180.0380.070-0.018—   
chr7_87463719_G_Tchr7:874637190.0380.055-0.018—   
chr7_87463994_C_Gchr7:874639940.017-0.0160.067—   
chr7_87464015_T_Cchr7:874640150.0000.0050.067—   
chr7_87464016_T_Achr7:874640160.0380.0390.031—   
chr7_87464016_T_Gchr7:874640160.0240.0180.067—   
chr7_87464019_T_Gchr7:87464019-0.038-0.0470.031—   
chr7_87464020_T_Gchr7:87464020-0.038-0.0390.037—   
chr7_87464021_T_Cchr7:874640210.0050.0160.067—   
chr7_87464043_C_Gchr7:874640430.0380.0230.037—   
chr7_87463601_A_Tchr7:874636010.0360.0360.058—   
chr7_87463615_A_Cchr7:874636150.0360.0650.055—   
chr7_87463627_A_Tchr7:87463627-0.036-0.013-0.058—   
chr7_87463703_T_Gchr7:87463703-0.036-0.0360.006—   
chr7_87463714_A_Tchr7:87463714-0.036-0.0390.006—   
chr7_87463715_G_Achr7:874637150.0030.068-0.064—   
chr7_87463719_G_Cchr7:874637190.0360.0390.009—   
chr7_87463996_A_Tchr7:874639960.0360.0620.031—   

Showing 200 of 200 in this window. Scores are the p99-scaled [−1, 1] value; click a column to sort.